1 |
Carbaglu |
- |
- |
- |
- |
245 [2] 245, 246 💬 |
2 |
Carglumic acid |
Carglumic acid |
[1] D07130 D07130 💬 |
CPS1 [1] CPS1 💬 |
Alanine, aspartate and glutamate metabolism [6] Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism |
245 [3] 245, 246, 251 💬 |
3 |
Carglumic acid (carbaglu®) |
Carglumic acid |
[1] D07130 D07130 💬 |
CPS1 [1] CPS1 💬 |
Alanine, aspartate and glutamate metabolism [6] Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism |
245 [2] 245, 246 💬 |
4 |
Cx-016492 |
- |
- |
- |
- |
245 [1] 245 💬 |
5 |
Cx-017950 |
- |
- |
- |
- |
245 [1] 245 💬 |
6 |
Disodium citrate |
- |
- |
- |
- |
245 [1] 245 💬 |
7 |
Glutamine |
L-Glutamine |
[1] D00015 D00015 💬 |
- |
- |
087 [7] 87, 89, 96, 97, 113, 245, 299 💬 |
8 |
Mrna-3927 |
- |
- |
- |
- |
245 [1] 245 💬 |
9 |
N-carbamylglutamate |
Carglumic acid |
[1] D07130 D07130 💬 |
CPS1 [1] CPS1 💬 |
Alanine, aspartate and glutamate metabolism [6] Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism |
245 [2] 245, 246 💬 |
10 |
Ornithine |
Ornithine |
[1] D08302 D08302 💬 |
- |
- |
245 [2] 245, 251 💬 |
11 |
Ornithine alpha ketoglutarate |
Ornithine |
[1] D08302 D08302 💬 |
- |
- |
245 [1] 245 💬 |
12 |
Other: standard of care |
- |
- |
- |
- |
013 [7] 13, 49, 64, 85, 96, 245, 246 💬 |
13 |
Standard of care treatment |
- |
- |
- |
- |
245 [2] 245, 246 💬 |