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薬物名(臨床試験情報から抽出)
DrugBank
KEGG DRUG
KEGG GENES
KEGG PATHWAY
指定難病告示番号
1
150-mg
IVACAFTOR
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
2
150mg
IVACAFTOR
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
3
75-mg
IVACAFTOR
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
4
CF patients with a G551D mutation and treated with
Ivacaftor
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
5
Deuterated
Ivacaftor
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
6
Elexacaftor /
Ivacaftor
/ Tezacaftor
3件:
Elexacaftor
Elexacaftor
,
Ivacaftor
,
Tezacaftor
3件:
D09916
D09916
(Name:
Ivacaftor
)
,
D11041
,
D11507
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
7
Elexacaftor 100 MG /
Ivacaftor
75 MG / Tezacaftor 50 MG, 2 tablets each morning +
Ivacaftor
150 mg one tablet each evening
Elexacaftor 100 MG /
Ivacaftor
75 MG / Tezacaftor 50 MG, 2 tablets each morning +
Ivacaftor
150 mg one
...
3件:
Elexacaftor
Elexacaftor
,
Ivacaftor
,
Tezacaftor
3件:
D09916
D09916
(Name:
Ivacaftor
)
,
D11041
,
D11507
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
8
Elexacaftor-tezacaftor-
ivacaftor
exposure
3件:
Elexacaftor
Elexacaftor
,
Ivacaftor
,
Tezacaftor
3件:
D09916
D09916
(Name:
Ivacaftor
)
,
D11041
,
D11507
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
9
Elexacaftor/tezacaftor/
ivacaftor
3件:
Elexacaftor
Elexacaftor
,
Ivacaftor
,
Tezacaftor
3件:
D09916
D09916
(Name:
Ivacaftor
)
,
D11041
,
D11507
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299
10
IVACAFTOR
1件:
Ivacaftor
Ivacaftor
1件:
D09916
D09916
(Name:
Ivacaftor
)
1件:
CFTR
CFTR
💬
8件:
ABC transporters
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic secretion
,
Tight junction
,
Vibrio cholerae infection
,
cAMP signaling pathway
💬
8件:
ABC transporters
,
AMPK signaling pathway
,
Bile secretion
,
Gastric acid secretion
,
Pancreatic sec
...
1件:
299
299