1 | BBP-671 | - | - | - | - | [2] 245 245, 246 |
2 | Carbaglu | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [2] 245 245, 246 |
3 | Carglumic Acid | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [3] 245 245, 246, 251 |
4 | Carglumic Acid (Carbaglu®) | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [2] 245 245, 246 |
5 | CX-016492 | - | - | - | - | [1] 245 245 |
6 | CX-017950 | - | - | - | - | [1] 245 245 |
7 | Disodium citrate | - | - | - | - | [1] 245 245 |
8 | Glutamine | [1] L-Glutamine L-Glutamine | [1] D00015
D00015
| - | - | [8] 87 87, 89, 96, 97, 113, 222, 245, 299 |
9 | HST5040 | - | - | - | - | [2] 245 245, 246 |
10 | MRNA-3927 | - | - | - | - | [1] 245 245 |
11 | N-Carbamylglutamate | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [2] 245 245, 246 |
12 | Ornithine | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [2] 245 245, 251 |
13 | Ornithine alpha ketoglutarate | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 245 245 |
14 | Standard of Care Treatment | - | - | - | - | [3] 53 53, 245, 246 |