1 | (1-13C) Sodium Acetate | [2] Acetate Acetate, Sodium acetate | [1] D01779
D01779
| - | - | [1] 251 251 |
2 | 15N ammonium chloride (15NH4Cl) | [2] Ammonium chloride Ammonium chloride, Chloride ion | [1] D01139
D01139
| - | - | [1] 251 251 |
3 | 4-phenylbutyrate | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [2] 251 251, 299 |
4 | AAVLK03hOTC | - | - | - | - | [1] 251 251 |
5 | Acetate | [1] Acetate Acetate | - | - | - | [41] 1 1, 2, 6, 10, 13, 46, 49, 51, 60, 64, 67, 70, 71, 73, 75, 76, 78, 79, 81, 83, 85, 86, 88, 90, 96, 97, 113, 145, 156, 171, 206, 222, 224, 225, 227, 235, 251, 265, 288, 298, 299 |
6 | Acetohydroxamic Acid | [1] Acetohydroxamic acid Acetohydroxamic acid | [1] D00220
D00220
| - | - | [1] 251 251 |
7 | Acetohydroxamic Acid Oral Tablet [Lithostat] | [1] Acetohydroxamic acid Acetohydroxamic acid | [1] D00220
D00220
| - | - | [1] 251 251 |
8 | Adenoviral Vector-Mediated Gene Transfer | - | - | - | - | [1] 251 251 |
9 | ALLOGENIC HUMAN HETEROLOGOUS LIVER CELLS | - | - | - | - | [1] 251 251 |
10 | Ammonium (15N) chloride | [1] Chloride ion Chloride ion | - | - | - | [1] 251 251 |
11 | Ammonium chloride | [2] Ammonium chloride Ammonium chloride, Chloride ion | [1] D01139
D01139
| - | - | [3] 96 96, 107, 251 |
12 | ARCT-810 | - | - | - | - | [1] 251 251 |
13 | Arginine | [1] Arginine Arginine | [1] D02982
D02982
| - | - | [11] 46 46, 58, 67, 78, 96, 97, 98, 113, 210, 251, 299 |
14 | ASA | - | - | - | - | [3] 13 13, 97, 251 |
15 | Avalotcagene ontaparvovec | [1] Avalotcagene ontaparvovec Avalotcagene ontaparvovec | - | - | - | [1] 251 251 |
16 | Carglumic Acid | [1] Carglumic acid Carglumic acid | [1] D07130
D07130
| [1] CPS1 CPS1 💬 | [6] Alanine, aspartate and glutamate metabolism Alanine, aspartate and glutamate metabolism, Arginine biosynthesis, Biosynthesis of amino acids, Carbon metabolism, Metabolic pathways, Nitrogen metabolism 💬 | [3] 245 245, 246, 251 |
17 | Celulas hepatocitos troncales adultas alogenicas de higado expandidas | - | - | - | - | [1] 251 251 |
18 | Chloride | [1] Chloride ion Chloride ion | - | - | - | [28] 6 6, 11, 13, 14, 34, 41, 46, 50, 51, 53, 60, 67, 70, 96, 97, 107, 127, 168, 171, 193, 227, 228, 251, 288, 296, 297, 299, 338 |
19 | DTX301 | - | - | - | - | [1] 251 251 |
20 | Ethanoate | [1] Acetic acid Acetic acid | [1] D00010
D00010
| - | - | [1] 251 251 |
21 | Glyceryl tri-(4-phenylbutyrate) | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [1] 251 251 |
22 | Glyceryl tri-(4-phenylbutyrate)(GT4P) | [2] Glycerol phenylbutyrate Glycerol phenylbutyrate, Phenylbutyric acid | [1] D10127
D10127
| - | - | [1] 251 251 |
23 | GT4P | [1] Glycerol phenylbutyrate Glycerol phenylbutyrate | [1] D10127
D10127
| - | - | [1] 251 251 |
24 | Heparesc | - | - | - | - | [1] 251 251 |
25 | HepaStem | - | - | - | - | [1] 251 251 |
26 | HepaStem Infusion | - | - | - | - | [1] 251 251 |
27 | Heterologous Human Adult Liver-derived Progenitor Cells | - | - | - | - | [1] 251 251 |
28 | Heterologous Human Adult Liver-derived Progenitor Cells (HHALPC) | - | - | - | - | [1] 251 251 |
29 | HHALPC | - | - | - | - | [1] 251 251 |
30 | HHLivC | - | - | - | - | [1] 251 251 |
31 | HPN-100 | - | - | - | - | [1] 251 251 |
32 | Human Heterologous Liver Cells | - | - | - | - | [1] 251 251 |
33 | Human heterologous liver cells (for infusion) | - | - | - | - | [1] 251 251 |
34 | Isotopic Intravenous [13C]-Urea | [1] Urea Urea | [2] D00023
D00023
,
D01749
| - | - | [1] 251 251 |
35 | KB195 | - | - | - | - | [1] 251 251 |
36 | MRNA encoding modified Ornithine transcarbamylase | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
37 | MRT5201 | - | - | - | - | [1] 251 251 |
38 | NaPBA | - | - | - | - | [1] 251 251 |
39 | Neo-ASA | - | - | - | - | [1] 251 251 |
40 | NITRIC OXIDE | [1] Nitric Oxide Nitric Oxide | [1] D00074
D00074
| - | - | [7] 85 85, 86, 88, 210, 251, 294, 299 |
41 | Nitric oxide supplement | [1] Nitric Oxide Nitric Oxide | [1] D00074
D00074
| - | - | [1] 251 251 |
42 | Oral corticosteroids | - | - | - | - | [5] 13 13, 46, 97, 171, 251 |
43 | Ornithine | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [2] 245 245, 251 |
44 | Ornithine transcarbamylase vector | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
45 | PHENYLBUTYRATE | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [12] 2 2, 3, 6, 8, 15, 93, 94, 244, 251, 297, 299, 338 |
46 | Promethera HepaStem | - | - | - | - | [1] 251 251 |
47 | Prophylactic Corticosteroid Taper Regimen | - | - | - | - | [1] 251 251 |
48 | RAVICTI | [1] Glycerol phenylbutyrate Glycerol phenylbutyrate | [1] D10127
D10127
| - | - | [2] 251 251, 299 |
49 | Reactive Corticosteroid Taper Regimen | - | - | - | - | [1] 251 251 |
50 | Recombinant adenovirus containing the ornithine transcarbamylase gene | [1] Ornithine Ornithine | [1] D08302
D08302
| - | - | [1] 251 251 |
51 | ScAAV8OTC | - | - | - | - | [1] 251 251 |
52 | Sodium acetate | [2] Acetate Acetate, Sodium acetate | [1] D01779
D01779
| - | - | [2] 81 81, 251 |
53 | Sodium acetate (1-13C) | [2] Acetate Acetate, Sodium acetate | [1] D01779
D01779
| - | - | [1] 251 251 |
54 | Sodium Ethanoate (1- 13 C) | [1] Acetic acid Acetic acid | [1] D00010
D00010
| - | - | [1] 251 251 |
55 | Sodium Ethanoate (1-13C) | [1] Acetic acid Acetic acid | [1] D00010
D00010
| - | - | [1] 251 251 |
56 | Sodium phenylbutyrate | [1] Phenylbutyric acid Phenylbutyric acid | - | - | - | [4] 2 2, 3, 8, 251 |
57 | SYNB1020 | - | - | - | - | [1] 251 251 |
58 | Urea | [1] Urea Urea | [2] D00023
D00023
,
D01749
| - | - | [2] 72 72, 251 |