1 | (S)-2-amino-6-(2-hydroxypropanoyl)-7,8-dihydropteridin-4(3H)-one | - | - | - | - | 1件: 240 240 💬 |
2 | 5,6,7,8-tetrahydrobiopterin | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
3 | 6R-BH4 | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 3件: 86 86, 124, 240 💬 |
4 | A16AX07 | - | - | - | - | 1件: 240 240 💬 |
5 | Amino acids | 1件: Amino acids Amino acids | - | - | - | 3件: 70 70, 240, 298 💬 |
6 | BH4 | - | - | - | - | 5件: 51 51, 86, 124, 240, 299 💬 |
7 | Blood samples | - | - | - | - | 9件: 13 13, 41, 51, 61, 97, 227, 240, 271, 280 💬 |
8 | BMN 165 | - | - | - | - | 1件: 240 240 💬 |
9 | BMN 165 (rAvPAL-PEG) | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
10 | BMN 307 | - | - | - | - | 1件: 240 240 💬 |
11 | BMN165 20mg/day | - | - | - | - | 1件: 240 240 💬 |
12 | BMN165 40mg/day | - | - | - | - | 1件: 240 240 💬 |
13 | CDX | - | - | - | - | 2件: 222 222, 240 💬 |
14 | CDX 6114 | - | - | - | - | 1件: 240 240 💬 |
15 | CNSA-001 | - | - | - | - | 1件: 240 240 💬 |
16 | Cohort 1 0.225g | - | - | - | - | 1件: 240 240 💬 |
17 | Cohort 2 0.75g | - | - | - | - | 1件: 240 240 💬 |
18 | Cohort 3 2.25 g | - | - | - | - | 1件: 240 240 💬 |
19 | Corn | 1件: Corn Corn | - | - | - | 2件: 46 46, 240 💬 |
20 | Corn/soy oil | 1件: Corn Corn | - | - | - | 1件: 240 240 💬 |
21 | Diet | - | - | - | - | 4件: 86 86, 97, 240, 299 💬 |
22 | Dietary Supplement for PKU patients | - | - | - | - | 1件: 240 240 💬 |
23 | Docosahexaenoic acid | 1件: Doconexent Doconexent | - | - | - | 7件: 6 6, 49, 90, 94, 240, 299, 301 💬 |
24 | Free amino acids intake | 1件: Amino acids Amino acids | - | - | - | 1件: 240 240 💬 |
25 | Glycomacropeptide-based protein substitute | - | - | - | - | 1件: 240 240 💬 |
26 | HMI-102 | - | - | - | - | 1件: 240 240 💬 |
27 | HMI-103 | - | - | - | - | 1件: 240 240 💬 |
28 | Immunosuppression | - | - | - | - | 1件: 240 240 💬 |
29 | KUVAN | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
30 | Kuvan 100mg soluble tablet | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
31 | KuvanTM Therapy | - | - | - | - | 1件: 240 240 💬 |
32 | Kuvan® | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
33 | Kuvan® (sapropterin dihydrochloride) | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
34 | Large Neutral Amino Acid Therapy | - | - | - | - | 1件: 240 240 💬 |
35 | Low calorie protein substitute | - | - | - | - | 1件: 240 240 💬 |
36 | Medikinet | - | - | - | - | 1件: 240 240 💬 |
37 | Moxifloxacin | 1件: Moxifloxacin Moxifloxacin | 1件: Moxifloxacin
Moxifloxacin
💬 | - | - | 9件: 2 2, 6, 46, 49, 85, 86, 113, 240, 299 💬 |
38 | N.a. | - | - | - | - | 10件: 3 3, 6, 8, 13, 46, 96, 97, 240, 256, 271 💬 |
39 | Nap | - | - | - | - | 2件: 96 96, 240 💬 |
40 | Palynziq | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
41 | PEG | - | - | - | - | 15件: 6 6, 13, 41, 46, 60, 65, 78, 96, 97, 140, 144, 240, 246, 299, 337 💬 |
42 | PEGVALIASE | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
43 | Pegvaliase-Pqpz | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
44 | Phenoptin | - | - | - | - | 2件: 124 124, 240 💬 |
45 | Phenylalanine | 1件: Phenylalanine Phenylalanine | 1件: Phenylalanine
Phenylalanine
💬 | - | - | 1件: 240 240 💬 |
46 | Phenylalanine restricted diet | 1件: Phenylalanine Phenylalanine | 1件: Phenylalanine
Phenylalanine
💬 | - | - | 1件: 240 240 💬 |
47 | Phenylalanine-free protein substitute in tablet form (XPhe minis) | 1件: Phenylalanine Phenylalanine | 1件: Phenylalanine
Phenylalanine
💬 | - | - | 1件: 240 240 💬 |
48 | Phenylalanine-free protein substitute tablets | 1件: Phenylalanine Phenylalanine | 1件: Phenylalanine
Phenylalanine
💬 | - | - | 1件: 240 240 💬 |
49 | Phenylketonuria-type diet | - | - | - | - | 1件: 240 240 💬 |
50 | PKU Explore | - | - | - | - | 1件: 240 240 💬 |
51 | PKU express plus | - | - | - | - | 1件: 240 240 💬 |
52 | PKU Sphere | - | - | - | - | 1件: 240 240 💬 |
53 | PKU sphere liquid | - | - | - | - | 1件: 240 240 💬 |
54 | PKU Start | - | - | - | - | 1件: 240 240 💬 |
55 | PKU/TYR GMP Protein Substitute | - | - | - | - | 1件: 240 240 💬 |
56 | Protein intake | - | - | - | - | 1件: 240 240 💬 |
57 | PTC923 | - | - | - | - | 1件: 240 240 💬 |
58 | RAvPAL-PEG | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
59 | RAvPAL-PEG 0.001 mg/kg | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
60 | RAvPAL-PEG 0.003 mg/kg | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
61 | RAvPAL-PEG 0.01 mg/kg | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
62 | RAvPAL-PEG 0.03 mg/kg | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
63 | RAvPAL-PEG 0.1 mg/kg | 1件: Pegvaliase Pegvaliase | 1件: Pegvaliase
Pegvaliase
💬 | 1件: PAH PAH 💬 | 5件: Biosynthesis of amino acids Biosynthesis of amino acids, Folate biosynthesis, Metabolic pathways, Phenylalanine metabolism, Phenylalanine, tyrosine and tryptophan biosynthesis 💬 | 1件: 240 240 💬 |
64 | RTX | - | - | - | - | 5件: 11 11, 46, 65, 222, 240 💬 |
65 | RTX-134 | - | - | - | - | 1件: 240 240 💬 |
66 | Sapropterin | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 3件: 86 86, 124, 240 💬 |
67 | Sapropterin (Kuvan) | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
68 | SAPROPTERIN DIHYDROCHLORIDE | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
69 | Sapropterin dihydrochloride, 6R-BH4, tetrahydrobiopterin | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
70 | Sapropterin Dihydrocholoride | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
71 | SAPROPTERIN HYDROCHLORIDE | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
72 | Sapropterin, sapropterin dihydrochloride | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
73 | Sapropterin, sapropterin hydrochloride | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
74 | Sapropterindihydrochloride | - | - | - | - | 1件: 240 240 💬 |
75 | Saproterin dihydrochloride | - | - | - | - | 1件: 240 240 💬 |
76 | SYNB1618 | - | - | - | - | 1件: 240 240 💬 |
77 | SYNB1934 | - | - | - | - | 1件: 240 240 💬 |
78 | Synergy | - | - | - | - | 1件: 240 240 💬 |
79 | T1401 | - | - | - | - | 1件: 240 240 💬 |
80 | Tetrahydrobiopterin | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |
81 | Tetrahydrobiopterin (BH4) | 1件: Sapropterin Sapropterin | 1件: Sapropterin
Sapropterin
💬 | - | - | 1件: 240 240 💬 |