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KEGG GENES
KEGG PATHWAY
KEGG DRUG
DrugBank
指定難病告示番号
1
EDNRB
💬
1. EDNRB
×
Name
Full Name
EDNRB
endothelin receptor type B
6件:
Calcium signaling pathway
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
,
Melanogenesis
,
Relaxin signaling pathway
,
Pathways in cancer
6件:
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
, ...
Bosentan
Bosentan
💬
1. EDNRB
×
Name
Other Names
Bosentan
Bosentan (USAN)
Bosentan hydrate (JAN)
Tracleer (TN)
ボセンタン水和物
トラクリア
ボセンタン
Bosentan
10件:
41
41
,
47
,
51
,
84
,
85
,
86
,
88
,
210
,
211
,
212
💬
1. EDNRB
×
告示番号
日本語名
英語名
41
巨細胞性動脈炎;側頭動脈炎
Giant cell arteritis
47
バージャー病;閉塞性血栓血管炎;ビュルガー病
Buerger disease
51
全身性強皮症
Scleroderma
84
サルコイドーシス
Sarcoidosis
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
88
慢性血栓塞栓性肺高血圧症;特発性慢性肺血栓塞栓症(肺高血圧型)
Chronic thromboembolic pulmonary hypertension
210
単心室症
Single Ventricle
211
左心低形成症候群
Hypoplastic left heart syndrome
212
三尖弁閉鎖症
Tricuspid atresia
2
EDNRB
💬
2. EDNRB
×
Name
Full Name
EDNRB
endothelin receptor type B
6件:
Calcium signaling pathway
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
,
Melanogenesis
,
Relaxin signaling pathway
,
Pathways in cancer
6件:
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
, ...
Bosentan
Bosentan
💬
2. EDNRB
×
Name
Other Names
Bosentan
Bosentan (INN)
ボセンタン
Bosentan
10件:
41
41
,
47
,
51
,
84
,
85
,
86
,
88
,
210
,
211
,
212
💬
2. EDNRB
×
告示番号
日本語名
英語名
41
巨細胞性動脈炎;側頭動脈炎
Giant cell arteritis
47
バージャー病;閉塞性血栓血管炎;ビュルガー病
Buerger disease
51
全身性強皮症
Scleroderma
84
サルコイドーシス
Sarcoidosis
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
88
慢性血栓塞栓性肺高血圧症;特発性慢性肺血栓塞栓症(肺高血圧型)
Chronic thromboembolic pulmonary hypertension
210
単心室症
Single Ventricle
211
左心低形成症候群
Hypoplastic left heart syndrome
212
三尖弁閉鎖症
Tricuspid atresia
3
EDNRB
💬
3. EDNRB
×
Name
Full Name
EDNRB
endothelin receptor type B
6件:
Calcium signaling pathway
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
,
Melanogenesis
,
Relaxin signaling pathway
,
Pathways in cancer
6件:
Calcium signaling pathway
,
cGMP-PKG signaling pathway
,
Neuroactive ligand-receptor interaction
, ...
Macitentan
Macitentan
💬
3. EDNRB
×
Name
Other Names
Macitentan
Macitentan (JAN/USAN)
Opsumit (TN)
マシテンタン
オプスミット
Macitentan
5件:
51
51
,
85
,
86
,
88
,
210
💬
3. EDNRB
×
告示番号
日本語名
英語名
51
全身性強皮症
Scleroderma
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
88
慢性血栓塞栓性肺高血圧症;特発性慢性肺血栓塞栓症(肺高血圧型)
Chronic thromboembolic pulmonary hypertension
210
単心室症
Single Ventricle
4
KIT
💬
4. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Dasatinib
Dasatinib
💬
4. KIT
×
Name
Other Names
Dasatinib
Dasatinib (JAN/INN)
ダサチニブ
Dasatinib
2件:
51
51
,
85
💬
4. KIT
×
告示番号
日本語名
英語名
51
全身性強皮症
Scleroderma
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
5
KIT
💬
5. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Dasatinib
Dasatinib
💬
5. KIT
×
Name
Other Names
Dasatinib
Dasatinib (USAN)
Dasatinib hydrate (JAN)
Sprycel (TN)
ダサチニブ水和物
スプリセル
Dasatinib
2件:
51
51
,
85
💬
5. KIT
×
告示番号
日本語名
英語名
51
全身性強皮症
Scleroderma
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
6
KIT
💬
6. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Imatinib
Imatinib
💬
6. KIT
×
Name
Other Names
Imatinib
Imatinib (INN)
Glamox (TN)
イマチニブ
Imatinib
12件:
13
13
,
28
,
34
,
35
,
46
,
51
,
85
,
86
,
87
,
88
,
89
,
162
💬
6. KIT
×
告示番号
日本語名
英語名
13
多発性硬化症/視神経脊髄炎
Multiple sclerosis/Neuromyelitis optica
28
全身性アミロイドーシス
Systemic amyloidosis
34
神経線維腫症
Neurofibromatosis
35
天疱瘡
Pemphigus
46
悪性関節リウマチ
Malignant rheumatoid arthritis
51
全身性強皮症
Scleroderma
85
特発性間質性肺炎
Idiopathic interstitial pneumonia
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
87
肺静脈閉塞症/肺毛細血管腫症
Pulmonary veno-occlusive disease
88
慢性血栓塞栓性肺高血圧症;特発性慢性肺血栓塞栓症(肺高血圧型)
Chronic thromboembolic pulmonary hypertension
89
リンパ脈管筋腫症
Lymphangioleiomyomatosis
162
類天疱瘡(後天性表皮水疱症を含む。)
Pemphigoid
7
KIT
💬
7. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Sorafenib
Sorafenib
💬
7. KIT
×
Name
Other Names
Sorafenib
Sorafenib (USAN/INN)
ソラフェニブ
Sorafenib
2件:
34
34
,
86
💬
7. KIT
×
告示番号
日本語名
英語名
34
神経線維腫症
Neurofibromatosis
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
8
KIT
💬
8. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Sunitinib
Sunitinib
💬
8. KIT
×
Name
Other Names
Sunitinib
Sunitinib (INN)
スニチニブ
Sunitinib
2件:
28
28
,
34
💬
8. KIT
×
告示番号
日本語名
英語名
28
全身性アミロイドーシス
Systemic amyloidosis
34
神経線維腫症
Neurofibromatosis
9
KIT
💬
9. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Nilotinib
Nilotinib
💬
9. KIT
×
Name
Other Names
Nilotinib
Nilotinib (USAN/INN)
ニロチニブ
Nilotinib
5件:
6
6
,
8
,
34
,
51
,
86
💬
9. KIT
×
告示番号
日本語名
英語名
6
パーキンソン病
Parkinson disease
8
ハンチントン病
Huntington disease
34
神経線維腫症
Neurofibromatosis
51
全身性強皮症
Scleroderma
86
肺動脈性肺高血圧症
Pulmonary arterial hypertension
10
KIT
💬
10. KIT
×
Name
Full Name
KIT
KIT proto-oncogene, receptor tyrosine kinase
11件:
MAPK signaling pathway
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signaling pathway
,
PI3K-Akt signaling pathway
,
Hematopoietic cell lineage
,
Melanogenesis
,
Pathways in cancer
,
Acute myeloid leukemia
,
Breast cancer
,
Central carbon metabolism in cancer
11件:
MAPK signaling pathway
,
Ras signaling pathway
,
Rap1 signaling pathway
,
Phospholipase D signalin
...
Masitinib
Masitinib
💬
10. KIT
×
Name
Other Names
Masitinib
Masitinib (INN)
マシチニブ
Masitinib
6件:
2
2
,
5
,
6
,
13
,
46
,
96
💬
10. KIT
×
告示番号
日本語名
英語名
2
筋萎縮性側索硬化症
Amyotrophic lateral sclerosis
5
進行性核上性麻痺
Progressive supranuclear palsy
6
パーキンソン病
Parkinson disease
13
多発性硬化症/視神経脊髄炎
Multiple sclerosis/Neuromyelitis optica
46
悪性関節リウマチ
Malignant rheumatoid arthritis
96
クローン病;回腸末端炎
Crohn disease